Table 1.

Levels of C6S (ng/ml) in patients with MPS IVA, IVB, and VII

Age (year)	Control	MPS IVA	MPS IVB	MPS VII
<3	156.7 ± 116.9 (n = 81)			940.7 (n = 1)
3–4	58.7 ± 17.4 (n = 20)	166.4 ± 83.8 (n = 2)
5–9	70.5 ± 17.1 (n = 18)	175.7 ± 87.2*** (n = 12)
10–14	66.1 ± 25.9 (n = 13)	141.7 ± 54.9*** (n = 8)	94.9 ± 6.2 (n = 2)
15–35	33.6 ± 19.2 (n = 6)	109.2 ± 45.0** (n = 11)	33.2 ± 6.8 (n = 2)	468.2 ± 533.8 (n = 2)
>36		103.7 ± 68.0 (n = 3)

Data represent the mean ± SD values

** and ***; significantly different from the control at p < 0.005, and 0.001, respectively