Table 2.

Levels of KS (μg/ml) in patients with MPS IVA, IVB, and VII

KS (μg/mL)	Control	MPS IVA	MPS IVB	MPS VII
<3	3.2 ± 0.9 (n = 81)			3.4 (n = 1)
3–4	3.2 ± 0.9 (n = 20)	3.0 ± 0.9 (n = 2)
5–9	2.9 ± 0.4 (n = 18)	4.3 ± 0.9*** (n = 12)
10–14	2.5 ± 1.1 (n = 13)	4.2 ± 1.2** (n = 8)	3.1 ± 0.1 (n = 2)
15–35	0.9 ± 0.3 (n = 6)	2.7 ± 0.9*** (n = 11)	1.3 ± 0.2 (n = 2)	2.4 ± 0.5 (n = 2)
>36		1.9 ± 1.0 (n = 3)

Data represent the mean ± SD values

** and ***; significantly different from the control at p < 0.005, and 0.001, respectively