Table 1.
Results of spirometry and body plethysmography, demonstrating forced expiratory volume in the 1st second in percent of expected value (FEV1%), forced ventilatory capacity in percent of expected value (FVC%), the ratio between FEV1 and FVC, and diffusing capacity of the lung for carbon monoxide in percent of expected value (DLCO%) and 6-minute walking tests in 7 patients with Hb Aalborg.
| Patient 1 (woman) | Patient 2 (man) | Patient 3 (woman) | Patient 4 (woman) | Patient 5 (woman) | Patient 6 (man) | Index person | |
|---|---|---|---|---|---|---|---|
| FEV1 (%) | 106 | 128 | 94 | 87 | 117 | 106 | 117 |
| FVC (%) | 108 | 122 | 103 | 107 | 104 | 98 | 134 |
| FEV1/FVC | 87 | 78 | 65 | 94 | 99 | 91 | 74 |
| DLCO (%) | 59 | 69 | 67 | 69 | 76 | 80 | 66 |
| Walking distance (m) | 417 | 480 | 562 | 420 | 568 | 551 | 273 |