Table 1.

Nomenclature for manifestations in different organ systems [adapted from Stone JH et al. A&R [[10]]]

Pancreas	IgG4-related pancreatitis (Type 1 autoimmune pancreatitis)
Bile ducts, gallbladder and liver	IgG4-related sclerosing cholangitis
	IgG4-related cholecystitis
	IgG4-related hepatopathy
Thyroid gland	IgG4-related thyroid disease
Salivary and lacrimal glands	IgG4-related sialadenitis
	IgG4-related parotitis
	IgG4-related submandibular gland disease
	IgG4-related dacryoadenitis
Orbits	IgG4-related ophthalmic disease
	IgG4-related orbital inflammatory pseudotumor
	IgG4-related pan-orbital inflammation
	IgG4-related orbital myositis
Retroperitoneal fibrosis, arteries	IgG4-related retroperitoneal fibrosis
	IgG4-related aortitis/periaortitis
	IgG4-related periarteritis
Intrapulmonary, mediastinal and pleural involvement	IgG4-related lung disease
	IgG4-related mediastinitis
	IgG4-related pleuritis
Lymph nodes	IgG4-related lymphadenopathy
Kidney	IgG4-related kidney disease
	tubulointerstitial nephritis secondary to IgG4-related disease
	membranous glomerulonephritis secondary to IgG4-related disease
	IgG4-related renal pyelitis
Miscellaneous	IgG4-related perineural disease*
	IgG4-related pachymeningitis
	IgG4-related hypophysitis
	IgG4-related mesenteritis
	IgG4-related mastitis
	IgG4-related prostatitis
	IgG4-related epididymo-orchitis*
	IgG4-related paratesticular pseudotumor*
	IgG4-related skin disease
	IgG4-related pericarditis