Table 1.
| Site of involvement | Manifestations | Percent of total PM |
| Upper extrathoracic and intrathoracic airways (larynx/glottis, trachea, mainstem bronchi) | Stenoses, tracheobronchitis, acute respiratory failure | 7%-8% |
| Large airways | Bronchiectasis | 23%-26% |
| Simple chronic bronchitis without suppuration | 10%-20% | |
| Mucoid impaction | ||
| Bronchial granulomas | ||
| Suppurative bronchitis | 3%-8% | |
| Small airways | Granulomatous bronchiolitis | 3%-10% |
| Acute bronchiolitis | ||
| Diffuse panbronchiolitis | ||
| Bronchiolitis obliterans syndrome | ||
| Concomitant diseases involving the airways | Asthma | |
| Chronic obstructive pulmonary disease | ||
| Sarcoidosis | ||
| A1 antitrypsin deficiency |
PM: Pulmonary manifestations.