Table 3.

Bowel pattern questionnaire in adult patients with Pompe disease and in age- and gender-matched controls (i.e. accompanying spouses and partners) as analysed by ICIQ-B-LF

	Pompe patients (n = 57)	Age- and gender-matched controls (n = 57)	p
Bowel pattern
Frequency	6.2 ± 3.5	4.2 ± 2.4	<0.001
Interference	7.5 ± 9.0	2.5 ± 4.4	<0.001
Bowel control
Frequency	5.6 ± 5.6	1.5 ± 2.0	<0.001
Interference	13.5 ± 16.2	1.9 ± 3.1	<0.001
Other bowel symptoms
Frequency	4.4 ± 2.3	3.8 ± 1.4	n.s.
Interference	5.0 ± 7.1	1.3 ± 2.7	<0.01
Sexual impact
Frequency	0.3 ± 1.1	0.02 ± 0.13	n.s.
Interference	0.4 ± 1.6	0.02 ± 0.13	n.s.
Quality of life
Frequency	3.7 ± 4.3	1.5 ± 2.2	0.02
Interference	11.5 ± 15.4	1.9 ± 5.0	<0.001

Data are given as mean ± 1SD. Groups were compared using Mann–Whitney rank sum test

n.s. nonsignificantly