Table 4.

Urinary incontinence in adult patients with Pompe disease and in age- and gender-matched controls (i.e. accompanying spouses and partners) as analysed by ICIQ-UI-SF

	Pompe patients (n = 58)	Age- and gender-matched controls (n = 58)	p
People reporting urinary incontinence [n (%)]b	23/55 (42)	14/56 (25)	n.s.
Frequency of urinary incontinencea	0.98 ± 1.45	0.43 ± 0.93	n.s.
Quantity of urinary incontinencea	1.15 ± 1.58	0.57 ± 1.06	n.s.
Interference with daily lifea	2.09 ± 3.15	0.48 ± 1.33	0.01
Interference with daily life in those patients reporting urinary incontinencea	5.00 ± 2.95	2.14 ± 2.07	0.004
Situations in which urinary incontinence occurs [n (%)]b,c
Never	32 (58)	37 (66)	n.s.
Before the toilet is reached	18 (33)	4 (7.1)	0.002
During coughing and pressure	3 (5.5)	15 (27)	0.0021
During sleeping	2 (3.6)	0	n.s.
During physical exertion	4 (7.3)	4 (7.1)	n.s.
After urinating and dressing	4 (7.3)	2 (3.6)	n.s.
Without explicable cause	3 (5.5)	2 (3.6)	n.s.
Permanently	0 (0)	0 (0)	n.s.

Data are given as mean ± 1SD. Groups were compared using Mann–Whitney rank sum test^a and Fisher exact test^b. ^cMore than one answer possible

n.s. nonsignificantly