Table 1.
Case | Sex | Ethnicity | Phenotype | Family history | Age at onset, years | Age at death, years | Cause of death |
---|---|---|---|---|---|---|---|
1 | F | American Caucasian | Non-manifesting | + | N/A | 89 | Natural |
2 | F | American Caucasian | Non-manifesting | + | N/A | 87 | Stroke |
3 | F | American Caucasian | Affected | - | ~9-10 | 77 | Complications of disorder |
4 | F | American Caucasian | Non-manifesting | + | N/A | 90 | Stroke |
5 | F | American Caucasian | Affected | + | N/A | 90 | Natural |
6 | F | American Caucasian | Non-manifesting | N/A | N/A | 88 | N/A |
7 | M | American Caucasian | Non-manifesting | N/A | N/A | 75 | Natural |
N/A: not available.