Figure 1. Family pedigree and relative audiograms.
Audiograms of family members were obtained using pure tone audiometery with air conduction at frequencies from 250 to 8000 Hz. The proband’s parents, II-2 at age 41 and II-3 at age 39, showed normal hearing audiograms, while the affected brothers, III-2 and III-3, showed severe to profound hearing loss.