Table 2.
n | (%) | ||
---|---|---|---|
Source of "gold standard" arteriopathy classification | |||
Vascular imaging review (normal, no arteriopathy review) | 116 | (32.7) | |
Arteriopathy diagnosis review | 239 | (67.3) | |
Baseline with clinical findings (Step 2) | 94 | (26.5) | |
Follow-up (Step 3) | 89 | (25.1) | |
Adjudication | 56 | (15.8) | |
Definite arteriopathy | 127 | (35.8) | |
Secondary diagnosis classified with high certainty* | 109 | (30.7) | |
Arterial dissection | 26 | (7.3) | |
Transient cerebral arteriopathy | 25 | (7.0) | |
Primary moyamoya | 17 | (4.8) | |
Secondary moyamoya | 17 | (4.8) | |
PHACES | 2 | (0.6) | |
Genetic arteriopathy | 4 | (1.1) | |
Primary vasculitis | 0 | (0) | |
Secondary vasculitis (including meningitis) | 15 | (4.2) | |
Iatrogenic | 1 | (0.3) | |
Fibromuscular dysplasia | 2 | (0.6) | |
Secondary diagnosis not further classified | 18 | (5.1) | |
Differential diagnosis includes:** | |||
Transient cerebral arteriopathy | 9 | (2.5) | |
Arterial dissection | 11 | (3.1) | |
Primary moyamoya | 4 | (1.1) | |
Secondary moyamoya | 0 | (0) | |
Genetic arteriopathy | 1 | (0.3) | |
Primary vasculitis | 2 | (0.6) | |
Secondary vasculitis (including meningitis) | 4 | (1.1) | |
Iatrogenic | 0 | (0) | |
Possible arteriopathy | 34 | (9.6) | |
Differential diagnosis includes:** | |||
Transient cerebral arteriopathy | 9 | (2.5) | |
Arterial dissection | 27 | (7.6) | |
Primary moyamoya | 1 | (0.3) | |
Secondary moyamoya | 0 | (0) | |
Genetic arteriopathy | 0 | (0) | |
Primary vasculitis | 1 | (0.3) | |
Secondary vasculitis (including meningitis) | 7 | (2.0) | |
Iatrogenic | 0 | (0) | |
Embolic (not arteriopathy) | 33 | (9.3) | |
No arteriopathy | 194 | (54.6) | |
No abnormalities on vascular imaging (no arteriopathy review) | 116 | (32.7) | |
Arteriopathy review | 78 | (22.0) | |
Classified as no arteriopathy, no embolus | 1 | (0.3) | |
Classified as no arteriopathy, low likelihood embolic | 2 | (0.6) | |
Classified as isolated occlusion, high likelihood embolic | 75 | (21.1) |
Sub-categories are mutually exclusive
Sub-categories are not mutually exclusive