Table 1. Summary of Reported Cases of Alien Hand Syndrome.
Reference | Case No. | Diagnosis | Localization of Lesion or Imaging Findings | Hand | Diagnostic Dyspraxia or Intermanual Conflict | Grasping | Levitation | Groping | Utilization Behavior |
---|---|---|---|---|---|---|---|---|---|
Goldstein69 | Infarction | L | X | X | |||||
Akelaitis70 | 1 | Callosotomy | Body of corpus callosum, genu of corpus callosum | L | X | ||||
2 | Callosotomy | Complete section of corpus callosum | R | X | |||||
Goldberg et al.71 | 1 | Infarction | L medial frontal cortex | R | X | X | X | ||
2 | Infarction | L medial frontal cortex | R | X | X | ||||
Levine and Rinn23 | Infarction | R temporal/occipital cortex, posterior thalamus | L | X | |||||
McNabb, et al.72 | Infarction | L superior and medial frontal cortex and parietal | R | X | X | ||||
Banks et al.36 | 1 | Gunshot wound | Medial frontal white matter bilaterally, corpus callosum, R basal ganglia, internal capsule and thalamus | L | X | ||||
2 | Ruptured anterior communicating Artery Aneurysm | Genu of corpus callosum, bilateral medial frontal cortex, R gyrus rectus | L | X | X | X | |||
Goldberg and Bloom73 | 1 | Infarction | Body of corpus callosum, R medial frontal cortex, supplementary motor area, anterior cingulate gyrus | L | X | X | X | ||
2 | Infarction | L medial frontal cortex, supplementary motor area, anterior cingulate gyrus | R | X | X | ||||
3 | Infarction | Corpus callosum, R medial frontal cortex, supplementary motor area, anterior cingulate gyrus | L | X | X | ||||
4 | Infarction | Corpus callosum, L medial posterior frontal cortex, supplementary motor area, anterior cingulate gyrus | R | X | X | ||||
Kuhn et al.74 | Infarction | Body of corpus callosum, genu of corpus callosum, bilateral anterior medial frontal cortex, supplementary motor area | R | X | |||||
Della Sala et al.75 | Ruptured anterior communicating artery aneurysm | Anterior corpus callosum, bilateral frontal cortex, L medial frontal cortex, supplementary motor area | R | X | X | ||||
Hanakita and Nishi76 | Infarction | Corpus callosum, L medial frontal cortex, cingulate gyrus | L | X | |||||
Feinberg et al.14 | Infarction | Corpus callosum, L medial frontal cortex | R | X | X | ||||
Gottlieb et al.77 | 1 | Possible corpus callosum, R fronto-parietal cortex | L | X | X | X | |||
2 | Body of corpus callosum, bilateral medial frontal cortex | L | X | ||||||
Leiguarda et al.39 | 1 | Idiopathic cortical atrophy | L medial frontal cortex atrophy | R | X | ||||
2 | Diffuse lymphocytic lymphoma | R medial frontal cortex | L | X | |||||
3 | Seizures after the removal of an arteriovenous malformation | L posterior parietal cortex | R | X | |||||
4 | Ruptured arteriovenous malformation | R parietal/temporal cortex | L | X | |||||
Dolado et al.78 | Infarction | Bilateral parietal | L | X | X | ||||
Green et al.79 | Alzheimer's Disease | R parietal cortex, mild frontal | L | ||||||
Ventura et al.80 | Hemorrhagic stroke | R capsulothalamic area, R frontal/temporal/parietal cortex | L | X | |||||
Geschwind et al.16 | Infarction | Body of corpus callosum, R cingulate cortex | L | X | |||||
Giroud and Dumas81 | 7 | Infarction | Corpus callosum, fronto-parietal ischemia | L | X | ||||
8 | Infarction | R anterior corpus callosum, R frontal cortex | L | X | |||||
Nagumo and Yamadori82 | Infarction | L body of corpus callosum, genu of corpus callosum | L | X | |||||
Papagno and Marsile83 | Ruptured Anterior Communicating Artery Aneurysm | Anterior corpus callosum, R medial frontal cortex | L | X | |||||
Chan et al.2 | Infarction | Body of corpus callosum, genu of corpus callosum, isthmus of corpus callosum, R supplementary motor area, anterior cingulate gyrus, bilateral medial prefrontal cortex | L | X | X | X | |||
Kischka et al.84 | Infarction | Anterior corpus callosum, L medial frontal cortex, parieto-occipital, supplementary motor area | R | X | X | X | |||
Tanaka et al.85 | 1 | Infarction | Post body of corpus callosum, anterior splenium of corpus callosum, L cingulate gyrus, temporoparietal | L | X | ||||
2 | Infarction | Body of corpus callosum, R cingulate gyrus, L anterior cingulate gyrus, bilateral medial frontal cortex | L | X | X | ||||
3 | Infarction | Body of corpus callosum, genu of corpus callosum, L anterior cingulate gyrus | L | X | |||||
4 | Infarction | Anterior body of corpus callosum, L medial frontal cortex, anterior cingulate gyrus | R | X | X | X | |||
5 | Infarction | Anterior body of corpus callosum, L medial frontal cortex | R | X | X | ||||
7 | Infarction | Anterior body of corpus callosum, R medial frontal cortex, anterior cingulate gyrus | L | X | X | X | |||
Andre and Domingues86 | Reversible ischemia | L internal capsule, R occipital cortex, L cerebellum | L | X | |||||
Chan and Ross87 | 1 | Infarction | Genu of corpus callosum, isthmus of corpus callosum, L medial frontal cortex, supplementary motor area, anterior cingulate gyrus | R, L | X (L) | X (R) | |||
2 | Infarction | Body of corpus callosum, genu of corpus callosum, R medial frontal cortex, supplementary motor area, anterior cingulate gyrus | L | X | X | ||||
3 | Infarction | Genu of corpus callosum–isthmus of corpus callosum, R prefrontal cortex, supplementary motor area, anterior cingulate gyrus | L | X | X | X | |||
Feinberg et al.9 | Seizures in the setting of a glioblastoma multiforme | R frontotemporal cortex | L | X | X | ||||
Nicholas et al.88 | Infarction with hemorrhagic conversion | Corpus callosum | L | X | X | ||||
Tow and Chua89 | Infarction | L medial frontal cortex and posterior parietal cortex | R | X | X | ||||
Ay et al.90 | Infarction | Splenium of corpus callosum, R posterior frontal/temporal/occipital/parietal cortex, thalamus | L | X | |||||
Groom et al.52 | Infarction | R medial posterior temporal cortex, posterior parietal/occipital cortex | L | X | |||||
Marti-Fabregas et al.91 | Infarction | R inferior parietal cortex | L | X | X | ||||
Fisher92 | 1 | Corticobasal syndrome | L, R | X (R) | X (L) | ||||
2 | Corticobasal syndrome | R | X | ||||||
3 | Corticobasal syndrome | L | X | X | |||||
4 | Corticobasal syndrome | L | X | ||||||
5 | Corticobasal syndrome | L, R | X (L) | X (both) | |||||
6 | Corticobasal syndrome | L | X | X | |||||
Ong Hai and Odderson93 | Infarction | Anterior corpus callosum, R medial frontal cortex | L | X | X | ||||
Bundick and Spinella43 | Infarction | R posterior parietal/temporal cortex, medial frontal cortex | L | X | |||||
Inzelberg et al.94 | Creutzfeld–Jakob disease | Mild cerebral atrophy | L | X | |||||
Carrilho et al.3 | 1 | Corticobasal syndrome | R temporal/parietal cortex | L | X | ||||
2 | Corticobasal syndrome | R temporal/parietal cortex | L | X | |||||
3 | Alzheimer's disease | L parietal cortex | R | X | |||||
4 | Infarction | R parietal cortex | L | X | |||||
Kumral27 | Moya-Moya leading to a hemorrhage | Body of corpus callosum, genu of corpus callosum, splenium of corpus callosum, R medial frontal cortex (unclear) | L | X | X | ||||
Nishikawa et al.95 | 1 | Infarction | Body of corpus callosum, genu of corpus callosum, splenium of corpus callosum | L | X | ||||
3 | Resection of a central neurocytoma via transcallosal and transcortical approaches | Anterior body of corpus callosum, splenium of corpus callosum, L parietal cortex | R | X | X | ||||
Lavados et al.96 | Hemorrhage | Corpus callosum, F medial (inferred) | L, R | X (L or R) | X (R) | X (R) | X (R) | ||
Suwanwela and Leelacheavasit97 | 1 | Infarction | Body of corpus callosum, splenium of corpus callosum | L | X | ||||
2 | Infarction | Body of corpus callosum | L | X | |||||
Marey-Lopez et al.50 | Infarction | R thalamus | L | X | X | ||||
Pack et al.68 | Infarction | R lateral thalamus | L | X | |||||
Rohde et al.20 | Presumed vascular-mediated cortical atrophy | L central/parietal cortical and subcortical lesions and extensive atrophy of the pre- and post-central gyri | R | X | |||||
Pappalardo et al.56 | Infarction | L cortical–subcortical parieto-occipital lobes | R | X | X | ||||
Giovannetti et al.37 | Infarction | L medial frontal extending into the corpus callosum | R | X | X | X | X | ||
Iwashita et al.98 | Infarction | R frontal lobe | L | ||||||
Espinosa et al.99 | Infarction | R parietal lobe and anterior corpus callosum | L | X | |||||
Kikkert et al.64 | 1 | Infarction | Presumed R parietal lesion | L | X | X | X | ||
2 | Infarction | L frontal lobe in the area of the anterior cerebral artery | R | X | X | ||||
Kurne et al.100 | Multiple Sclerosis | Non-enhancing multiple hyperintense lesions in the corpus callosum, periventricular white matter and centrum semiovale on MRI | L | X | |||||
Caixeta101 | HIV | R frontal and parietal hypodensity on CT | L | X | X | X | |||
Bejot et al.102 | Infarction | Bilateral hyperintense signals in diffusion-weighted images in the anterior cerebral artery territories involving the R anterior corpus callosum | L | X | |||||
Kessler et al.47 | Infarction | L anterior parietal lobule and posterior lip of post-central gyrus | R | X | |||||
Soman et al.103 | Infarction | R parietal lobe, dorsal putamen, and body of caudate | L | X | |||||
Spector et al.24 | Infarction | R parietal lobe | L | X | |||||
Haq et al.61 | Brain herniation | R cerebral peduncle gliosis and L cystic anterior thalamus changes | R | X | X | ||||
Takenouchi and Solomon11 | Parry Romberg Syndrome | Progressive atrophy and gliosis of the R thalamus | L | X | X | ||||
Kim et al.104 | Infarction | R parietal | L | X | X | ||||
Faber et al.105 | Infarction | L paracallosal area | R | X | |||||
Terazzi et al.106 | Infarction | R thalamus and calcarine cortex | L | X | X | X | |||
Cantagallo et al.65 | Hemorrhage | Fronto-basal area bilaterally, L fronto-opercolar area and L frontal superior area | R | X | |||||
Prakash et al.19 | Corticobasal syndrome | Asymmetrical R fronto-parietal cortical atrophy | L | X | |||||
Pooyania et al.62 | Infarction | L superior frontal gyrus | R | X | X | X | |||
Bartolo et al.51 | Infarction | L posterior thalamus, parahippocampal gyrus, inferior and posterior temporal lobe, lateral portion of the splenium of the corpus callosum, and cortical part of the occipital lobe. | R | X | X | ||||
Yuan et al.22 | Infarction | Genu, body and splenium of the corpus callosum | L | X | |||||
Verleger et al.42 | Infarction | L side of corpus callosum from genu to posterior isthmus | L | X | |||||
Huang and Jia15 | Cerebral venous malformation | Hemorrhage in the genu and body of the corpus callosum | L | X | |||||
Nandhagopa et al.17 | Infarction | Bilateral parietal parasagittal areas initially, body of corpus callosum found to be involved later | L | X | |||||
Rubin et al.26 | 1 | Creutzfeld–Jakob disease | Diffuse cortical T2 signal on MRI | L | |||||
2 | Creutzfeld–Jakob disease | Normal | L | ||||||
3 | Creutzfeld–Jakob disease | Bilateral striatum, diffuse cortex left hemisphere | R | ||||||
4 | Creutzfeld–Jakob disease | Normal | L | ||||||
5 | Creutzfeld–Jakob disease | Unknown | L | ||||||
6 | Creutzfeld–Jakob disease | R posterior parietal cortical hypoattenuation on CT | L | ||||||
7 | Creutzfeld–Jakob disease | Normal imaging | R | ||||||
8 | Creutzfeld–Jakob disease | Cortical and striatal DWI/FLAIR hyperintensity Diffusely on MRI | L | ||||||
9 | Creutzfeld–Jakob disease | Bilateral L> R selective parietal restricted diffusion on MRI | R | ||||||
10 | Creutzfeld–Jakob disease | Restricted diffusion in bilateral striatal nuclei, left parietal cortex on MRI | R | ||||||
11 | Creutzfeld–Jakob disease | Diffuse restricted diffusion, T2 hyperintensity of R posterior hemispheric cortex on MRI | L | ||||||
12 | Creutzfeld–Jakob disease | Restricted diffusion, T2 hyperintensity of bilateral R> L parietal, occipital lobes on MRI | L | X | X | ||||
13 | Creutzfeld–Jakob disease | Diffuse cortical restricted diffusion on MRI | L | ||||||
Nash et al.7 | Pneumocephalus | R frontal lobe | L | X | |||||
Hertz et al.107 | Infarction | L posterior middle cerebral artery territory infarction | R | X | |||||
Park et al.1 | 1 | Infarction | L medial frontal white matter infarction | R | X | ||||
2 | Infarction | R frontal lobe and anterior corpus callosum infarction | L | X | |||||
Shereef and Cavanna48 | Infarction | R posterior parietal | L | ||||||
Jang et al.41 | Infarction | Anterior portion of the L cingulated gyrus and the corpus callosum (posterior portion of the genu to the anterior portion of the splenium) | R | X | X | X | |||
Graff-Radford et al.46 | 108 cases | Corticobasal syndrome | |||||||
14 cases | Cerebrovascular | Ischemic strokes, arteriovenous malformation and subdural hematoma | |||||||
9 cases | Creutzfeld–Jakob disease | ||||||||
5 cases | Hereditary Diffuse Leukoencephalopathy with Spheroids | ||||||||
4 cases | Tumor | Astrocytomas and oligodendroglioma | |||||||
10 cases | Other | ||||||||
McBride et al.38 | Corticobasal syndrome | Asymmetric atrophy of L parietal regions | R | X | |||||
Nowak et al.67 | 1 | Infarction | L anterior corpus callosum, left anterior paramedian periventricular white matter and adjacent paramedian cortex | R | X | X | X | ||
2 | Infarction | L anterior corpus callosum and overlying white matter | R | X | X | ||||
Lunardelli et al.108 | Multiple Sclerosis | Multiple corpus callosal lesions, especially of caudal portion | L | X | |||||
Chokar et al.109 | Cerebral vasculitis | R hemispheric cortical and subcortical edema affecting the white matter and temporal, parietal, and occipital lobes | L | X | |||||
Romano et al.66 | Hemorrhage | L fronto-parietal hemorrhage | R | X | X |
Abbreviations: CT, Catscan; DWI, Diffusion-weighted Imaging; FLAIR, Fluid-attenuated Inversion Recovery; HIV, Human Imunodeficiency Virus; L, Left; MRI, Magnetic Resonance Imaging; R, Right; X, finding present in that case.