Table 1.
Clinical findings in the three patients
Characteristic | Case 1 | Case 2 | Case 3 |
---|---|---|---|
Age (years) | 52 | 65 | 74 |
Gender | Male | Male | Female |
Location of rash | B, E, N | B, E, F | E |
Duration of rash (years) | 0.2 | 2 | 4 |
Body temperature (°F) | 102° | 102.2° | 98.0° |
Hemoglobin (g/dL) | 9.2 | 9.5 | 9.5 |
Hematocrit | 28.4% | 28.9% | 28.5% |
White blood cell count (×109/L) | 35.4 | 1.2 | 9.4–>19.2 |
Neutrophils | 92% | 54% | 76%–>83% |
Lymphocytes | 4% | 46% | 16% |
Blasts | 2% | 0% | 0% |
Platelet count (×109/L) | 70 | 113 | 300 |
Bone marrow blasts | 45% | 0% | <1% |
Dermal biopsy | Sweet syndrome | Sweet syndrome | Sweet syndrome |
Associated malignancy | AML | Hairy cell leukemia | MGUS, CLL/SLL |
B indicates back; E, extremity; F, face; N, neck; AML, acute myelogenous leukemia; MGUS, monoclonal gammopathy of uncertain significance; CLL/SLL, chronic lymphocytic leukemia/small lymphocytic lymphoma.