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. 2014 Dec 3;7:66. doi: 10.1186/s12920-014-0066-9

Table 3.

Results from urinary test of glycosaminoglycan related parameters

Urinary test Value (sister) Value (brother) Reference value Result Unit
Urinary glycosaminoglycan (GAG) 528.1 413.8 0 abnormal mg/L
Urinary glycosaminoglycan/Creatinine (GAG/Cr) 36.7 39.7 <8.4 abnormal mg/mmol
Dermatan sulfate + + - abnormal
Heparan sulfate + + - abnormal
Keratan - - - normal
Chondroitin sulfate - - - normal