Table 1.

Treatment responses of attacks in the proband and other affected family members

	Age	Age at onset of Pl/Dyst attacks	Duration of Pl/Dyst attacks	Monthly frequency of Pl/Dyst attacks	Triggers (alleviating factors) of Pl/Dyst attacks	Current therapy, age at outset [previous therapy, age at outset]	Attack-free periods: age of onset, duration	Age at end of Pl /Dyst attacks
Proband	4 years 8 months	2 years/ 8 months	Mins to 15 days/mins to 2 days	2 to 4/2	Exercise, stress (sleep)/ exercise +++, fever	MAD, 3 years 5 months		3 years 5 months/ 3 years 5 months
Mother	27 years	2 years/ 2 months	NA/ mins to hours	NA/4	NA/ exercise +++ (rest, sleep)	PHT, 8 years [CZP, 13 months]; [FNR, 7 years]	Age 8 years, 4 months Age 7 years, 6 months	5 ½ years/ ongoing
Maternal uncle	25 years	2 years/8 years	NA/ mins to hours	30 then 4/10 to 20	Exercise/ exercise +++	FNR, 2 years 9 months; PHT, 6 years		5 years/ ongoing
Maternal grandmother	52 years	3 years/ NA	5 min to 1 hour/ 30 min to hours	NA/4	NA/exercise +++ (rest)	PB, < 30 years; PHT, 34 years [CZP, < 30 years]; [FNR, 32 years]; [other AEs]		NA/ ongoing

Abbreviations: Pl plegic, Dyst dystonic, MAD Modified Atkins Diet, AE antiepileptic drug, CZP carbamazepine, FNR flunarizine, PB Phenobarbital, PHT phenytoin, NA not available, +++ usual trigger