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. Author manuscript; available in PMC: 2016 Jan 1.
Published in final edited form as: Mol Genet Metab. 2014 Nov 8;114(1):55–61. doi: 10.1016/j.ymgme.2014.11.001

Table 3.

Summary of extracellular and intracellular purine nucleotides level.

Phenotype LND HND HRH normal
Intracellular purines (nmol/mg protein)
AMP 0.39 ± 0.24 0.64 ± 0.92 0.63 ± 0.56 0.56 ± 0.45
GDP 0.61 ± 0.16 0.73 ± 0.36 0.81 ± 0.20 0.75 ± 0.22
ADP 3.34 ± 0.78 3.94 ± 1.87 4.05 ± 1.15 4.14 ± 1.28
GTP 8.09 ± 1.40 8.97 ± 1.53 8.92 ± 1.59 7.85 ± 2.00
ATP 24.38 ± 3.54 26.70 ± 4.17 25.98 ± 3.76 25.71 ± 5.17

Extracellular purines (μmol/mg protein)
Hypoxanthine 0.51 ± 0.12 0.62 ± 0.26 0.49 ± 0.19 0.23 ± 0.10
Xanthine 0.42 ± 0.10 0.43 ± 0.19 0.44 ± 0.13 0.34 ± 0.09
Uric acid 0.36 ± 0.11 0.39 ± 0.19 0.37 ± 0.11 0.27 ± 0.13
Adenine 0.21 ± 0.05 0.25 ± 0.09 0.21 ± 0.07 0.17 ± 0.04