Table 2.

Cochleo-vestibular malformations as classified by Sennaroglu and Saatci [20]

Malformation	Characteristics
Labyrinthine aplasia	Complete absence of cochlea and vestibule
Cochlear aplasia	Cochlea absent, vestibule present
Common cavity	Cochlea and vestibule are represented by a single, undifferentiated cystic cavity
Incomplete partition type 1	Cystic-appearing cochlea lacking entire modiolus and cribriform area; large cystic vestibule
Cochlear hypoplasia	Cochlea and vestibule smaller than normal
Incomplete partition type 2	Cochlea consists of 1.5 turns (normally it has 2.5 turns); middle and apical turns coalesce to form a cystic apex