Table 1.

Causes of PH by group

WHO group1	n (%)
I (PAH)	23 (76%)
‐idiopathic/heritable	14
‐congenital heart disease	4
‐connective tissue disease	3
‐portopulmonary hypertension	1
‐hemolytic disorder	1
II (Heart disease)	2 (7%)
‐left ventricular diastolic dysfunction	2
III (Lung disease)	2 (7%)
‐COPD	2
IV (CTEPH)	1 (3%)
V (miscellaneous)	2 (7%)
‐sarcoidosis	2

CTEPH = chronic thromboembolic pulmonary hypertension; PAH = pulmonary arterial hypertension.