Table 2.
| A. Disease course in patients undergoing resection. | ||
|---|---|---|
| Atypical | Typical | |
| Recurrent disease | 26 (41%) | 3 (1%)a |
| Risk of recurrence by initial stage, median years to recurrence (range) | ||
| IA | 7 of 29 (24%), 3.7 (0.9–32) | 0 |
| IB | 4 of 5 (80%), 4.8 (2.9–5) | 0 |
| IIA | 6 of 12 (50%), 3.5 (1–6.4) | 0 |
| IIB | 1 of 4 (25%), 0.4 | 0 |
| IIIA | 8 of 14 (57%), 3.1 (1.2–11.6) | 1 (33%, 8) |
| IIIB | N/A | 0 |
| B. Sites of metastasis noted on imaging for patients either at presentation or recurrence. | ||
|---|---|---|
| Atypical (n = 34) |
Typical (n = 14) |
|
| Adrenal | 2 (6%) | – |
| Bone | 18 (53%) | 2 (14%) |
| Brain | 6 (18%) | – |
| Liver | 27 (79%) | 1 (7%) |
| Lung, contralateral | 1 (3%) | 11 (79%)a |
| Pancreas | 2 (6%) | – |
| Soft tissue | 3 (9%) | – |
| Spleen | 2 (6%) | – |
a
Initial stage at diagnosis unavailable for 2 patients.
a
Cannot exclude synchronous or metachronous tumors.