Table 3.

Previously reported pediatric-type sarcoma in adults and children

Type	No.	Study years	Results	Reference
Western
RMS
Adults	1,071	1973-2005	Adults with RMS had significantly worse outcome than children, tumors were more likely to be at unfavorable site; 5-year survival rate 27% vs. 61%	Sultan et al., 2009 [3]
Children	1,529
Adults	171	1975-2001	Overall rate of response to chemotherapy was 85%; 5-year event-free survival was 28% and 5-year overall survival was 61%	Ferrari et al., 2003 [18]
Adults	113		5-Year survival rate 26%	Ariel and Briceno, 1975 [19]
EWS/PNET
Age ≤ 14	190	1972-1992	Rate of relapse ≤ 14 years vs. >14 years: 15.9 vs. 13.8 (p < 0.94)	Bacci et al., 2004 [13]
Age > 14	212
Adults Children	19	1995-2003	Median OS of patients ≤ 20 years vs. > 20 years did not differ (p=0.27)	Yamada et al., 2006 [14]
Adults	372	1989-2007	Adult age, hispanic race, metastatic disease, large tumor size, low socioeconomic status are poor prognostic factors for overall survival	Lee et al., 2010 [12]
Children	353
Adults	24	1990-2005	Localized disease: 3-year survival 59%	Gupta et al., 2010 [20]
Adults	27	1979-2002	5-Year survival rate 58%	Smorenburg et al., 2007 [5]
Adults	25	1991-2002	Axial location: 2-year survival 33%	Argon et al., 2004 [21]
Children	220	1979-2004	5-Year survival rate 63.5%	Rodriguez-Galindo et al., 2007 [22]
DSRCT
Adults	18	1998-2006	5-Year survival rate 27.9%	Liping et al., 2008 [23]
Asian
Adults	84	1995-2009	Median OS 33.1 months	Ahn et al., 2011 [24]
			Median EFS 14.4 months
			Localized disease was a significant independent prognostic factor for longer OS, and favorable primary tumor sites were associated with longer EFS