Table 2. Enzymatic analysis of activities of OXPHOS complexes in fibroblasts.
| Cell line | Description | CI | CII | CIII | CIV | CV | CII+CIII (SCC) |
|---|---|---|---|---|---|---|---|
| P1 | CII deficient | 98.7 | 47.6 | 269.7 | 233.5 | 275.2 | 36.9 |
| P2 | CII deficient | 119.2 | 12.6 | 308.3 | 209.9 | 255.9 | 18.5 |
| P3 | CII deficient | 86.6 | 37.9 | 270.0 | 215.6 | 275.3 | 30.9 |
| P4 | CII deficient | 120.7 | 46.3 | 286.8 | 230.5 | 200.8 | 29.8 |
| C | Control | 110.3 | 189.2 | 277.7 | 238.5 | 209.2 | 89.4 |
| P5 | CI deficient | 24.4 | 174.3 | 236.5 | 226.9 | 200.5 | 101.8 |
| P6 | CI deficient | 20.6 | 207.6 | 285.8 | 255.8 | 226.9 | 138.2 |
| Control range | 35–243 | 80–277 | 135–416 | 64–451 | 88–420 | 43–162 |
Activities are expressed in mU per mg protein. Numbers are averages from duplicate measurements that each were within a 10% range of their average. Numbers in bold are below the control range.