Table 1.
Reported cases of pancreas PEComas and symptoms at diagnosis.
Case | Sex | Age | Position | Size (mm) | Symptoms | |
---|---|---|---|---|---|---|
1 | Zamboni et al. (1996) [2] | F | 60 | Body | 20 | Abdominal pain |
2 | Heywood et al. (2004) [4] | F | 74 | Head | 45 | Abdominal pain |
3 | Ramuz et al. (2005) [5] | F | 31 | Body | 15 | Abdominal pain |
4 | Périgny et al. (2008) [6] | F | 46 | Body | 17 | Diarrhea |
5 | Hirabayashi et al. (2009) [7] | F | 47 | Head | 17 | Abdominal pain |
6 | Baez et al. (2009) [8] | F | 60 | Body | 32 | Bulge in right upper quadrant |
7 | Zemet et al. (2011) [9] | M | 49 | Head | 32 | Fever, cough, and malaise |
8 | Nagata et al. (2011) [10] | M | 52 | Head | 40 | Abdominal pain |
9 | Finzi et al. (2012) [11] | F | 62 | Head | 25 | No symptoms |
10 | Al-Haddad et al. (2013) [12] | F | 38 | Uncinate process | 18 | Abdominal pain |
11 | Okuwaki et al. (2013) [13] | F | 43 | Body | 100 | Abdominal pain |
12 | Our patient | F | 17 | Head | 42 | Melena |
| ||||||
12 patients | 10F/2M | Mean age 48 (range 17–74) |
Body: 5 Head: 6 Uncinate process: 1 |
Mean 36 mm (range 15–100 mm) |
Abdominal pain: 7 Bulge: 1 Nonspecific symptoms: 2 GI bleeding: 1 No symptoms: 1 |