Table 1.

Demographic characteristics and laboratory assessments of Italian C1-INH-HAE patients

	Type I	Type II	Total
Patients (%)	859 (87%)	124 (13%)	983
Gender (M/F)	407/452	55/69	462/521
Median age (years)	44	45	45
Median age at diagnosis (years)	25	31	26
Antigenic C1-INH, median value (%)	21 (IR 13-25)	96 (IR 64-150)	24 (IR 14-31)
Funcitional C1-INH, median value (%)	20 (IR 10-30)	19 (IR 10-30)	20 (IR 10-30)
Antigenic C4, median value (%)	20 (IR 10-25)	21(IR 12-30)	20 (IR 11-26)