FIG. 1.

Complete cryptophthalmos. Various clinical presentations of complete cryptophthalmos. A, Typical complete cryptophthalmos with total absence of the eyelids, eyebrow, eyebrow hairs, and a centrally located normal sized globe. B, A medially displaced globe with total absence of the eyebrow and eyebrow hairs except laterally. A skin tag is seen lateral to the globe. Note ipsilateral absence of the nasal cavity. C, A failed previous reconstruction attempt in a patient with complete cryptophthalmos showing an enlarged proptotic centrally located globe with total absence of the eyebrow ipsilateral to the defect and a contralateral tongue of hair replacing the eyebrow—underlies the difficulty in managing these patients. A previous cleft lip repair is also seen ipsilateral to the cryptophthalmic eye. Note the contralateral microphthalmic globe. D, CT scan of the same patient showing the globe replaced by a figure-of-eight cystic lesion to which normally sized extraocular muscles are attached posteriorly. Note the widening of the superior orbital fissure and the defect in the greater wing of the sphenoid. (*) This globe did not react to light shown through the skin in contrast to the contralateral microphthalmic globe that showed some reaction to light.