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. 2014 Dec 2;3(6):e001236. doi: 10.1161/JAHA.114.001236

Table 3.

All‐Cause Mortality in the Unit for Cardiac and Cardiovascular Genetics Registry

Attained Age (y) Observed Deaths Expected Deaths SMR 95% CI
Both sexes
0 to 19 2 1.66 1.21 0.30 to 4.83
20 to 39 11 9.00 1.22 0.68 to 2.21
40 to 59 34 33.05 1.03 0.73 to 1.44
60 to 69 29 33.14 0.88 0.61 to 1.26
70 to 79 20 33.29 0.60* 0.39 to 0.93
>80 17 19.85 0.86 0.53 to 1.38
Total 113 130.01 0.87 0.72 to 1.05
0 to 69 76 76.88 0.99 0.79 to 1.24
Men
0 to 19 2 1.12 1.78 0.45 to 7.13
20 to 39 6 6.11 0.98 0.44 to 2.19
40 to 59 17 19.25 0.88 0.55 to 1.42
60 to 69 20 19.54 1.02 0.66 to 1.59
70 to 79 7 17.01 0.41* 0.20 to 0.86
>80 7 5.52 1.27 0.60 to 2.66
Total 59 68.58 0.86 0.67 to 1.11
0 to 69 45 46.05 0.98 0.73 to 1.31
Women
0 to 19 0 0.53 0
20 to 39 5 2.89 1.73 0.72 to 4.15
40 to 59 17 13.80 1.23 0.77 to 1.98
60 to 69 9 13.60 0.66 0.34 to 1.27
70 to 79 13 16.28 0.80 0.46 to 1.38
>80 10 14.33 0.70 0.38 to 1.30
Total 54 61.44 0.88 0.67 to 1.15
0 to 69 31 30.83 1.01 0.71 to 1.43

SMR indicates standardized mortality ratio.

*

P<0.05.