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. Author manuscript; available in PMC: 2015 Aug 1.
Published in final edited form as: Neurol Clin. 2014 Aug;32(3):647–viii. doi: 10.1016/j.ncl.2014.04.009

Table 2. Comparison of KU SANM group with prior literature.

Grable-Esposito et al. 2010 KU
Cases 25 11
Mean age of onset(yrs) 64.7 55
Female/male ratio 1.1/1 2.6/1
Phenotype Proximal arm and leg Proximal leg mainly
Bulbar symptoms 3 2
Post-statin D/C weakness for > 1month >2 month
Mean CK 8203 5700
Autoimmune d/o & Abnormal labs Hashimoto thyroiditis ANA (2) - Jo1 (1), ANA (1) and RF
# RX with immunosupressants 22 10