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. Author manuscript; available in PMC: 2015 Mar 3.
Published in final edited form as: Mol Genet Metab. 2014 Jan 13;111(3):382–389. doi: 10.1016/j.ymgme.2014.01.002

Table 5.

β-Hexosaminidase activities using the fluorometric method on plasma.

Parameter Normal range (0–1 yr) Normal range (1–3 yr) Affected patient average
Total Hex 390–2622 532–1748 14.5
HexB 50–1458 267–995 0
%HexA 13–56 24.1–52.2 100

β-Hexosaminidase activities are presented as µmol/h/l of blood.