Table 1.
Types and distribution of interstitial lung disease and connective tissue disease†
| Characteristics | ILD (n=1256) |
No ILD (n=2317) |
||||
|---|---|---|---|---|---|---|
| UIP 551 (44%) |
NSIP 74 (6%) |
OP 70 (6%) |
LIP 4 (<1%) |
PF-NOS 557 (44%) |
||
| CTD (n=450) | 29 (9%) | 35 (11%) | 19 (6%) | 2 (<1%) | 241 (74%) | 124 (5%) |
| RA | 8 (28%) | 6 (17%) | 3 (16%) | 0 (0%) | 64 (27%) | 62 (50%) |
| PM/DM | 4 (14%) | 7 (20%) | 5 (26%) | 0 (0%) | 27 (11%) | 6 (5%) |
| SSc | 3 (10%) | 6 (17%) | 2 (11%) | 0 (0%) | 59 (24%) | 13 (10%) |
| SLE | 0 (0%) | 2 (6%) | 0 (0%) | 1 (50%) | 13 (5%) | 6 (5%) |
| MCTD | 7 (24%) | 7 (20%) | 2 (11%) | 1 (50%) | 48 (20%) | 14 (11%) |
| Sjögren | 2 (7%) | 3 (9%) | 1 (5%) | 0 (0%) | 9 (4%) | 11 (9%) |
| UCTD | 5 (17%) | 4 (11%) | 6 (31%) | 0 (0%) | 21 (9%) | 12 (10%) |
| No CTD (n=3123) | 522 (56%) | 39 (4%) | 51 (6%) | 2 (<1%) | 316 (34%) | 2193 (95%) |
†
ILD, interstitial lung disease; CTD, connective tissue disease; UIP, usual interstitial pneumonia; NSIP, nonspecific interstitial pneumonia; OP, organizing pneumonia; LIP, lymphoid interstitial pneumonia; PF-NOS, pulmonary fibrosis non-otherwise specified or unclassifiable; RA, rheumatoid arthritis; PM/DM, poly-/dermatomyositis; SSc, systemic sclerosis; SLE, systemic lupus erythematosus; MCTD, mixed connective tissue disease; UCTD, undifferentiated connective tissue disease