TABLE 1.
Demographics and Follow-up of JPS Patients (n = 41)
| Patients With Upper GI Tract Biopsies (n = 22) | |||
|---|---|---|---|
| Patients Without Upper GI Tract Biopsies (n = 19) |
Without Upper JP (n = 9) |
With Upper JP (n = 13) |
|
| Sex (male, female) | 8, 11 | 4, 5 | 4, 9 |
| Race (white, black, other) | 13, 4, 2 | 8, 1, 0 | 12, 1, 0 |
| Family history (yes, no, unknown) | 7, 5, 7 | 4, 4, 1 | 8, 1, 4 |
| Gene mutation | Unknown | Unknown | 2 patients with SMAD4 mutation |
| Total colectomy | 9 | 5 | 6 |
| Total gastrectomy | 0 | 0 | 3 |
| GI tract Adenocarcinoma | 1 colorectum | 0 | 1 stomach |
| Death | 1 | 0 | 3 |
| Age at first pathology specimen (y) | 11.7 (2.5–33) | 12.0 (3–26) | 30.5 (4–68) |
| Age at last pathology specimen (y) | 14.6 (4–35) | 15.4 (8–27) | 38.2 (7–73) |
| Pathology follow-up/patient (mo) | 31.3 (1–96) | 36.6 (5–97) | 93.5 (4–171) |
| No. upper endoscopies/patient (average, range) | 2 patients had normal EGD without biopsy | 1.2 (1–2) | 4.5 (1–12) |
| Age at first EGD specimen (y) | NA | 13.4 (4–26) | 31.5 (6–73) |
| Age at last EGD specimen (y) | NA | 13.8 (6–26) | 37.5 (7–73) |
| EGD follow-up/patient (mo) | NA | 3.9 (1–17) | 73.2 (1–150) |
| Age at first upper JP diagnosis (y) | NA | NA | 33.4 (7–73) |
Data shown in the table are average and range.