Table 1.

Classification of vasculitides associated with neuropathy (according to Collins et al. [2010]).

Primary systemic vasculitis
1. Small vessel vasculitis
Microscopic polyangiitis
Eosinophilic granulomatosis with polyangiitis (Churg–Strauss syndrome)
Granulomatosis with polyangiitis (GPA)
Essential mixed cryoglobulinemic (non-Hepatitis C)
Henoch–Schönlein purpura
2. Medium vessel vasculitis
Polyarteritis nodosa
3. Large vessel vasculitis
Giant cell arteritis
Secondary systemic vasculitis
1. Connective tissue diseases
➢ Rheumatoid arthritis
➢ Systemic lupus erythematosus
➢ Sjögren’s syndrome
➢ Systemic sclerosis
➢ Dermatomyositis
➢ Mixed connective tissue disease
2. Sarcoidosis
3. Behcet’s disease
4. Infections (hepatitis B and C, HIV, cytomegalovirus and others)
5. Drugs
6. Malignancy
7. Inflammatory bowel disease
8. Hypocomplementemic urticarial vasculitis syndrome
Nonsystemic or localized vasculitis
1. Nonsystemic vasculitic neuropathy
2. Diabetic radiculoplexus neuropathy (DRPLN)
3. Localized cutaneous or neuropathic vasculitis