Table 2.

Frequency of neuropathy in vasculitic diseases.

Disease	Frequency	Reference
Primary systemic vasculitis
Giant cell arteritis	Rare	[Chia et al. 1996; Koike et al. 2013]
Polyarteritis nodosa	65–85%	[Schaublin et al. 2005; Ohyama et al. 2013b]
Churg–Strauss syndrome	65–80%	[Hattori et al. 1999; Zwerina, 2008]
Granulomatosis with polyangiitis	5–50%	[Schaublin et al. 2005; De Souza et al. 2010]
Microscopic polyangiitis	6–75%	[Hattori et al. 2002; Schaublin et al. 2005]
Cryoglobulinemia	30–70%	[Cacoub et al. 2008; Collins and Periquet, 2008]
Secondary systemic vasculitis
1. Connective tissue diseases
Systemic lupus erythematosus	20–27%	[Vital et al. 2006; Servioli et al. 2007]
Rheumatoid arthritis	15–70%	[Voskuyl et al. 2003; Agarwal et al. 2008; Muramatsu et al. 2008]
Sjögren’s syndrome	30–45%	[Delalande et al. 2004; Terrier et al. 2007]
Systemic sclerosis (scleroderma)	5–30%	[Dyck et al. 1997; Collins and Periquet, 2008]
2. Others
Infections (hepatitis B virus, hepatitis C virus (HCV), HIV)	5–70%	[Said and Lacroix, 2005; Schaublin et al. 2005; Cacoub et al. 2008; Collins and Periquet, 2008, Ohyama et al. 2013b]
Sarcoidosis	5–10%	[Chen and McLeod, 1989; Allen et al. 2003; Vital et al. 2008]
Malignancy	Rare*	[Oh et al. 1991; Fain et al. 2007]
Drugs	Rare	[Schapira et al. 2000; Thaisetthawatkul et al. 2011]