Table 2.
Demographics of Patients With Airway-Related Surgery.
| Hurler | Hurler-Scheie | Scheie | Alla | |
|---|---|---|---|---|
| Patients reporting at least 1 airway-related surgery | 246 | 99 | 45 | 403 |
| Median age at diagnosis, y | 1.1 | 4.0 | 8.3 | 1.4 |
| Range | −0.6-11.3 | −0.4-11.6 | 0-40.3 | −0.6-43.9 |
| Median number of airway-related surgeries per patient | 1.0 | 2.0 | 1.0 | 1.0 |
| Range | 1.0-14.0 | 1.0-7.0 | 1.0-3.0 | 1.0-14.0 |
| Number of patients with a known surgery date and diagnosis date | 242 | 93 | 43 | 390 |
| Age at first airway surgery, y | 2.0 | 4.7 | 5.5 | 3.0 |
| Range | 0-14.4 | 0.1-21.1 | 0.8-18.8 | 0-21.1 |
| Percentage of patients with airway surgery before diagnosis | 11.2 | 34.4 | 65.1 | 22.3 |
| Total number of airway-related surgeries | 440 | 178 | 64 | 698 |
a
Includes patients with unknown phenotype.