Table 1.
Demographic and clinical characteristics of PFAPA patients.
Total number of patients | 81 |
Male | 50 (63%) |
Female | 31 (37%) |
Age at disease onset (mean ± SD, range) | 2.1 ± 1.5 years (0.1–6.5 years) |
Age at diagnosis (mean ± SD, range) | 3.9 ± 1.7 years (1.2–7 years) |
Interval between disease onset and diagnosis (mean ± SD, range) | 1.9 ± 1.5 years (0.4–6.5 years) |
Duration of febrile episode (mean, range) | 4.2 days (2–11 days) |
Interval between episodes (mean, range) | 4 weeks (14–60 days) |