Immunocytochemical analysis of HeLa cells transiently transfected with wild-type or
mutant cochlins. Cochlin localization was detected by immunostaining with an Alexa
555-conjugated anti-HA antibody (red). The ER and Golgi complex were immunostained with
Alexa 488 (green) using anti-KDEL and anti-Golgin-97 antibodies, respectively. Nuclei were
counterstained with DAPI (cyan). Wild-type, p.G87W, p.P89H, p.V104del, p.I109T, p.A119T,
and p.F121S each colocalized with the ER and Golgi complex markers, but both p.C162Y and
p.A487P did not colocalize with the Golgi complex markers, indicating lack of transport of
these mutant cochlins from ER to the Golgi apparatus.