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. 2015 Apr 10;10(4):e0121799. doi: 10.1371/journal.pone.0121799

Table 1. Clinical data of all SMA patients sorted by age.

ID Type Age at inclusion (years) Weight (kg) Height (cm) Time spent in the wheelchair (months) Arthrodesis FVC (%) NNV Tracheo- stomy Brooke score (#)
703 SMA III 8.3 27 121 45 no 79 no no 2
203 SMA II 10.7 23 134 129 no 43 no no 3
502 SMA III 10.7 57 163 NA no 69 no no 2
708 SMA II 11.2 49 140 135 no NA no no 4
323 SMA II 12.4 25 NA 149 yes 49 yes no 2
326 SMA II 12.5 50 159 151 yes 39 yes no 5
321 SMA II 13.2 22 146 158 yes 22 yes no 4
909 SMA II 13.6 37 145 163 yes NA no no 2
709 SMA II 13.8 42 147 165 yes 27 yes no 4
318 SMA II 15.3 52 161 184 yes 70 no no 3
315 SMA II 15.4 37 141 185 yes 24 yes no 6
320 SMA II 15.5 37 155 187 yes 16 no no 5
512 SMA II 16.1 50 149 193 yes 24 yes no 6
907 SMA II 16.6 47 150 199 yes NA yes no 4
506 SMA III 17.5 117 154 90 NA 48 no no 3
908 SMA II 18.9 29 130 227 yes 31 no no 4
503 SMA III 19.9 30 175 143 yes NA no no 3
107 SMA III 21.8 65 179 82 no 100 no no 3
121 SMA II 24.8 NA NA 298 yes 16 no no 5
905 SMA II 26.0 40 158 312 yes NA no yes 3
118 SMA III 27.4 51 162 149 no 78 no no 3
120 SMA III 29.9 52 163 311 yes NA NA NA 5
113 SMA II 31.0 35 150 372 NA NA NA NA 3

FVC—Forced vital capacity (% of predicted values), NNV—nasal nocturnal ventilation, NA- not available.