Table 5.
Fifty Operative procedures classified according to preoperative knowledge of vEDS diagnosis
| N=50 (%) | Diagnosis Known N=29 |
Diagnosis not known N=21 |
P* |
|---|---|---|---|
| Family History | 13 (44.8) | 9 (42.9) | .890 |
| Haploinsufficiency Mutation | 6 (20.7) | 7 (33.3) | .314 |
| Open Surgical Repair | 14 (48.3) | 17 (81.0) | .019 |
| Endovascular Procedures | 15 (51.7) | 4 (19.0) | .019 |
| Emergent Repairs | 12 (41.3) | 17 (80.9) | .005 |
| Intraoperative Death | 0 | 3 (14.2) | .036 |
| Post-operative complications | 4 (13.7) | 13 (61.9) | <.001 |
P value calculated using the Pearson Chi-square test for categorical data