Table 1.

Diagnosis of types 1, 2, 3, and idiopathic HAE

Laboratory test	Type 1 HAE	Type 2 HAE	Type 3 and idiopathic HAE
C4 concentration	Low	Low	Normal
C1-INH concentration	Low	Normal/high	Normal
C1-INH function	Low	Low	Normal

Abbreviations: C1-INH, C1-inhibitor; HAE, hereditary angioedema.