Table 1.
Cases of reversible pulmonary hypertension (PH) with multiple myeloma (MM) or smoldering MM (SMM)
| Diagnosis date | ||||||||
|---|---|---|---|---|---|---|---|---|
| Case | Age at diagnosis, years | SMM or MM | PH | MM type | Plasma cells, % | M-spike, g/dL | Other | PH (RVSP), mmHg |
| 1 | 63 | 9/19/2007 | 2007 | IgG λ | 20–30 | 2.1 | Sleep apnea, membranoproliferative glomerulonephritis | 84 |
| 2 | 59 | 4/28/2003 | 2004 | IgG κ | 10 | 1.4 | Scleromyxedema | 106 |
| 3a | 58 | 11/11/1996 | 1996 | IgG κ | 10–15 | 1.02 | Dermatomyositis | 105 |
| 4b | 31 | 3/2003 | 2003 | IgG λ | 80 | 3.3 | … | 80 |
RVSP: right ventricular systolic pressure; IgG: immunoglobulin G.
Previous Mayo Clinic case.
Italy case.