Skip to main content
. Author manuscript; available in PMC: 2015 May 4.
Published in final edited form as: Circulation. 2010 Dec 15;123(4):e18–e209. doi: 10.1161/CIR.0b013e3182009701

Table 8-4.

Surgery for Congenital Heart Disease

Sample Population,
Weighted
Surgery for congenital heart disease, n 14 888 25 831
Deaths, n 736 1253
Mortality rate, % 4.9 4.8
By sex (81 missing in sample)
  Males 8127 14 109
    Deaths, n 420 714
    Mortality rate, % 5.2 5.1
  Females 6680 11 592
    Deaths, n 315 539
    Mortality rate, % 4.7 4.6
By type of surgery
  ASD secundum surgery, n 834 1448
    Deaths, n 3 6
    Mortality rate, % 0.4 0.4
  Norwood procedure for HPLHS, n 161 286
    Deaths, n 42 72
    Mortality rate, % 26.1 25.2

ASD indicates atrial septal defect; HPLHS, hypoplastic left heart syndrome.

In 2003, 25 000 cardiovascular operations for congenital cardiovascular defects were performed on children <20 years of age. Inpatient mortality rate after all types of cardiac surgery was 4.8%. Nevertheless, mortality risk varies substantially for different defect types, from 0.4% for ASD repair to 25.2% for first-stage palliation for HPLHS. Fifty-five percent of operations were performed in males. In unadjusted analysis, mortality after cardiac surgery was somewhat higher for males than for females (5.1% versus 4.6%).

Source: Analysis of 2003 Kids’ Inpatient Database, HCUPnet, Healthcare Cost and Utilization Project, Agency for Healthcare Research and Quality (http://www.hcup-us.ahrq.gov), and personal communication with Kathy Jenkins, MD, Children’s Hospital of Boston, October 1, 2006.