Table 2.
Clinical features at the time of (1) SCE and (2) neuropsychological examination. The two most dominant clinical features are shown in bold
| Clinical feature | (1) SCE (n = 81) N (%) patients affected | (2) Neuropsychological examination (n = 30) N (%) patients affected |
|---|---|---|
| Cognitive complaint | 72 (89) | 22 (73) |
| Ataxia | 63 (78) | 16 (53) |
| Anxiety/depression | 32 (39) | 7 (23) |
| Speech difficulty | 28 (35) | 6 (20) |
| Personality change1 | 28 (35) | 10 (33) |
| Apraxia | 28 (35) | 8 (27) |
| Myoclonus | 26 (32) | 6 (20) |
| Extra-pyramidal signs | 19 (23) | 5 (17) |
| Hallucinations/delusions | 19 (23) | 4 (13) |
| Pyramidal signs | 17 (21) | 1 (3) |
| Sensory Disturbance | 17 (21) | 1 (3) |
| Diarrhea | 2 (2) | 1 (3) |
SCE, short cognitive examination.
1
Aggressivity/irritability; withdrawal/loss of drive; emotional lability.