Table 1.
Past case reports of fibronectin glomerulopathy
| Reporter | Case numbers | Age at biopsy (years) | Pcr at biopsy (µmol/L) | Proteinuria (at biopsy) | Renal outcome (Follow-up years) |
|---|---|---|---|---|---|
| Strom et al. [6] | 23 patients (6 families) | 14–59 | 45.8–137 | 21 patients: positive (9 patients: nephrotic) | 4 patients: HD (2,7,10,13 years) |
| Gemperle et al. [1] | 9 patients (1 family) | 20–46 | Not reported | 7 patients: positive, (1 patient: nephrotic) | 2 patients: HD (14, 14), 2 patients: CAPD (15,21 years) |
| Castelletti et al. [4] | 8 patients (1 family) | 12–59 | 53.4–168 | 6 patients: positive (4 patients: nephrotic), 2 patients: unknown | HD(-) (max. follow-up: 23 years) |
| Uesugiet al. [7] | 5 patients (4 families) | 3–75 | 15.3–122 | 5 patients: positive (2 patients: nephrotic) | HD(-) (max. follow-up: 10 years) |
| Sato et al. [8] | 1 patient | 23 | 68.6 | 1–2 g/day | not reported |
| Niimi et al. [9] | 1 patient | 3 | 15.3 | Nephrotic | Pcr was stable (7 years) |
| Nadamuni et al. [10] | 1 patient | 50 | 61.0 | Nephrotic | Pcr was stable (1 year) |
| Baydar et al. [11] | 1 patient | 24 | 62.5 | 1 g/day | Pcr was stable (2.5 years) |
| This Case | 1 patient | 78 | 99.1 | 6.8 g/day | HD |
Pcr, Plasma creatinine.