Table 2.
Survival of patients with various histologic subtypes
| Histology | n | % | PFS [months, (95% CI)] | OS [months, (95% CI)] |
|---|---|---|---|---|
| Leiomyosarcoma | 9 | 20.9 | 5.6 (2.7-8.5) | 9.9 (5.3-14.4) |
| Angiosarcoma | 6 | 14.0 | 3.2 (2.1-4.2) | 8.0 (3.7-12.4) |
| MFH/UPS | 5 | 11.6 | 7.1 (0.3-13.8) | 7.5 (1.1-13.9) |
| MPNST | 5 | 11.6 | 6.5 (0.7-12.3) | 8.9 (3.5-14.3) |
| Fibroblastic tumor | 4 | 9.3 | 5.7 (0.7-10.8) | 6.4 (1.6-11.2) |
| Synovial sarcoma | 4 | 9.3 | 7.7 (3.5-11.9) | 9.4 (4.4-14.5) |
| Rhabdomyosarcoma | 3 | 7.0 | 0.9 (0.5-1.3) | 2.5 (0.7-4.4) |
| Liposarcoma | 2 | 4.7 | 1.3 (0.7-1.9) | 1.5 (1.1-1.8) |
| Tumor of uncertain differentiation | 3 | 7.0 | 1.4 (0.5-2.3) | 4.1 (−0.4-8.5) |
| Desmoplastic small cell tumor | 1 | 2.3 | 10.3 (N/A) | 43.4 (N/A) |
| PEComa | 1 | 2.3 | 3.8 (N/A) | 4.1 (N/A) |
| Total | 43 | 100 | 5.0 (3.6-6.4) | 8.2 (5.8-10.6) |
PFS = progression-free survival, CI = confidence interval, OS = overall survival, MFH/UPS = malignant fibrous histiocytoma/undifferentiated pleomorphic sarcoma, MPNST = malignant peripheral nerve sheath tumor, PEComa = perivascular epithelioid cell tumor; N/A, not available.