Table 1.
Clinical features of the patients before lung biopsy and after treatment*
Disease, patient/age | Clinical features before lung biopsy
|
Clinical features after treatment
|
||||||||
---|---|---|---|---|---|---|---|---|---|---|
Disease duration, years | Subtype | Anti–topo I | Tobacco use | MRSS | FVC, % predicted | DLco, % predicted | FibMax | FVC, % predicted | FibMax | |
NSIP | ||||||||||
1/42 | 3 | dcSSc | + | No | 23 | 72 | NA | 2 | NA | 5 |
2/50 | 15 | dcSSc | + | Former | 15.5 | 88 | NA | 10 | 53 | NA |
3/44 | 10 | dcSSc | – | Former | 45 | 68 | 77 | NA | 60 | 13 |
4/41 | 8 | dcSSc | – | No | 24 | 70 | 44 | 4 | NA | 5 |
5/27 | 1 | lcSSc | – | No | 19 | 84 | 51 | 5 | 73 | 12 |
6/55 | 16 | lcSSc | – | No | 12 | 61 | 45 | 9 | 80 | 16 |
7/53 | 7 | lcSSc | – | No | 5 | 55 | 38 | 14 | 48 | NA |
8/57 | 6 | dcSSc | – | No | 21 | 84 | 59 | NA | 86 | NA |
9/43 | 1 | dcSSc | – | No | 46 | 78 | NA | 7 | 73 | 31 |
10/46 | 4 | lcSSc | + | No | 10 | 70 | NA | 7 | 38 | 16 |
11/45 | 1 | lcSSc | – | No | 0 | 74 | 91 | 7 | 75 | 8 |
12/24 | 13 | dcSSc | + | No | 34.5 | 68 | 74 | 2 | 64 | NA |
13/30 | 7 | lcSSc | – | Yes | 17 | 74 | NA | 18 | 75 | 14 |
14/57 | 9 | lcSSc | + | No | 7 | 61 | NA | 5 | 88 | 9 |
15/40 | 6 | dcSSc | + | No | 16 | 70 | 63 | 2 | 51 | 13 |
16/41 | 2 | dcSSc | + | No | 28.5 | 65 | 74 | 2 | NA | NA |
CLF | ||||||||||
1/38 | 5 | lcSSc | + | No | 4 | 48 | 39 | NA | NA | NA |
2/48 | 3 | dcSSc | + | No | 27 | 54 | 41 | 5 | NA | NA |
3/53 | 23 | lcSSc | – | No | 13.5 | 81 | 89 | NA | 105 | NA |
4/51 | 13 | lcSSc | – | No | 6.5 | 76 | 66 | 7 | 60 | 10 |
5/31 | 3 | dcSSc | + | No | 12 | 81 | 67 | 11 | 86 | 14 |
Anti–topo I = anti–topoisomerase I; MRSS = modified Rodnan skin thickness score; FVC = forced vital capacity; DLco = diffusing capacity for carbon monoxide; FibMax = sum of all scores in 6 lung zones; NSIP = nonspecific interstitial pneumonia; dcSSc = diffuse cutaneous systemic sclerosis; NA= not available; lcSSc = limited cutaneous systemic sclerosis; CLF= centrilobular fibrosis.