Table 2.
Risk (%) | Disorder | Treatment |
---|---|---|
Highest (up to 60) | ||
MGD + Y + intra-abdominal | Gonadectomy at diagnosis (all) | |
Fraiser | ||
Denys–Drash + Y | ||
PAIS + intra-abdominal | ||
Intermediate (up to 28) | ||
Turner + Y | Gonadectomy at diagnosis | |
MGD + Y + scrotal | Examination every 6 months + | |
PAIS Scrotal gonad | pubertal biopsy + | |
17β-hydroxylase | irradiation if CIS | |
Lowest (5) | ||
Ovotestis DSD | Gonadectomy at puberty Testicular tissue removal | |
Genetically confirmed CAIS |