Table 1. Diagnosis of IgG4-related disease.
Diseases | No. of cases | Definite (%) | Probable (%) | Possible (%) |
---|---|---|---|---|
IgG4-RD | 132 | 111 (84) | 3 (2) | 18 (14) |
AIP | 85 | 72 (85) | 3 (3) | 10 (12) |
SC | 12 | 11 (92) | 0 | 1 (8) |
DAC | 38 | 36 (95) | 0 | 2 (5) |
SIA | 56 | 50 (89) | 0 | 6 (11) |
LYM | 20 | 19 (95) | 0 | 1 (5) |
RF | 19 | 17 (89) | 0 | 2 (11) |
KD | 6 | 6 (100) | 0 | 0 |
PT | 3 | 3 (100) | 0 | 0 |
AIP, autoimmune pancreatitis; SC, IgG4-related sclerosing cholangitis; DAC, IgG4-related dacryoadenitis; SIA, IgG4-related sialadenitis; LYM, IgG4-related lymphadenopathy; RF, IgG4-related retroperitoneal fibrosis; KD, IgG4-related kidney disease; PT, IgG4-related pseudotumor.