Table 3. Clinical feature of each organ for IgG4-related disease.
| Features | IgG4-RD | AIP | SC | DAC | SIA | LYM | RF | KID | PT |
|---|---|---|---|---|---|---|---|---|---|
| No. association | 132 | 85 | 12 | 38 | 56 | 20 | 19 | 6 | 3 |
| Single lesion | 67 | 49 | 3 | 3 | 7 | 2 | 2 | 0 | 1 |
| Multiple lesion | 65 | 36 | 9 | 35 | 49 | 18 | 17 | 6 | 2 |
| Double lesions | 36 | 17 | 6 | 16 | 24 | 2 | 6 | 1 | 0 |
| Triple lesions | 19 | 13 | 2 | 10 | 15 | 9 | 6 | 2 | 0 |
| Four lesions | 8 | 4 | 1 | 8 | 8 | 5 | 3 | 2 | 1 |
| Five lesions | 1 | 1 | 0 | 1 | 1 | 1 | 1 | 0 | 0 |
| Six lesions | 1 | 1 | 0 | 0 | 1 | 1 | 1 | 1 | 1 |
| Rate (%) | 0 | 42 | 75 | 92 | 88 | 90 | 89 | 100 | 67 |
| Serum levels | |||||||||
| IgG4 (mg/dL) | 548.3 | 491.0 | 568.0 | 724.8 | 821.3 | 979.0 | 769.1 | 524.5 | 600.0 |
| IgG (mg/dL) | 2,094.2 | 2,082.0 | 2,402.0 | 2,107.8 | 2,432.8 | 2,687.4 | 2,526.8 | 1,838.3 | 1,967.0 |
| Treatment | |||||||||
| Steroid | 82 | 60 (71%) | 10 (83%) | 21 (55%) | 30 (54%) | 7 (35%) | 13 (68%) | 5 (83%) | 1 (33%) |
| Observation | 36 | 15 | 1 | 17 | 22 | 12 | 6 | 1 | 0 |
| Operation | 14 | 10 | 1 | 0 | 4 | 1 | 0 | 0 | 2 |
AIP, autoimmune pancreatitis; SC, IgG4-related sclerosing cholangitis; DAC, IgG4-related dacryoadenitis; SIA, IgG4-related sialadenitis; LYM, IgG4-related lymphadenopathy; RF, IgG4-related retroperitoneal fibrosis; KD, IgG4-related kidney disease; PT, IgG4-related pseudotumor.