Table 1.
Characteristic | Age, y (Sex) | Location |
Outcome (Time From Diagnosis to Death, mo) | Reference | ||
---|---|---|---|---|---|---|
Brain | Liver | Other | ||||
Patients without known risk factors | ||||||
Country of origin | ||||||
South Korea | 11 (F) | No | Yes | No | Death (14) | [9] |
South Korea | 28 (M) | Yes | No | No | Death (0.5) | [10] |
Turkey | 8 (M) | No | Yes | LN | Death (7) | [17] |
Turkey | 24 (F) | No | Yes | LN | Cure | [11] |
China | 3 (M) | Yes | No | No | Death (4) | [12] |
China | 19 (F) | Yes | No | LN | Death (5) | [13] |
China | 30 (F) | Yes | No | No | Death (0.1) | [13] |
China | 3 (F) | Yes | No | No | Death (6) | [13] |
China | 19 (F) | Yes | No | LN | Death (1) | [8] |
China | 21 (F) | No | Yes | LN | Cure | [7] |
Japan | 25 (F) | No | No | Palate, LN | Death (36) | [6] |
Japan | 30 (F) | Yes | No | LN | Death (3) | [6] |
Japan | 11 (M) | No | Yes | LN, dig | Death (ND) | [6] |
Japan | 14 (F)a | No | Yes | No | Death (2) | [6] |
Japan | 5 (F)a | Yes | No | No | Death (1) | [6] |
Japan | NA (F) | Yes | No | No | Death (ND) | [6] |
Japan | 26 (F) | Yes | No | No | Death (9) | [6] |
Japan | 19 (M)a | Yes | Yes | LN | Death (2) | [6] |
Japan | NA (M)a | Yes | Yes | NA | Death (ND) | [6] |
Japan | 10 (M) | Yes | No | Lung | Death (11) | [6] |
Japan | 20 (M) | Yes | No | LN | Death (NA) | [6] |
Japan | 17 (M) | Yes | Yes | LN | Death (48) | [6] |
Pakistan | 70 (M) | Yes | No | No | Death (0.5) | [18] |
Patients with predisposing factors other than PID | ||||||
Predisposing factor | ||||||
Contaminated steroid use | 77 (F) | Yes | No | No | Death | [5] |
Contaminated steroid use | 61 (F) | Yes | No | No | Cure | [5] |
Contaminated steroid use | 71 (F) | Yes | No | No | ND | [5] |
Contaminated steroid use | 65 (F) | Yes | No | No | ND | [5] |
Contaminated steroid use | 52 (F) | Yes | No | No | ND | [5] |
Bronchiectasis | 81 (M) | No | No | Lung | Cure | [15] |
Lung cancer, catheter use | 58 (F) | No | No | Blood | Cure | [5] |
CAPD, catheter use | 55 (M) | No | No | Peritoneal | Cure | [5] |
CAPD, catheter use | 39 (M) | No | No | Peritoneal | Cure | [5] |
ALL | 62 (F) | No | No | LN | Cure | [5] |
Cystic fibrosis | 29 (F) | No | No | Lung | Cure | [5] |
Cystic fibrosis | 6 (F) | No | No | Lung | Cure | [5] |
Cystic fibrosis | 54 (F) | No | No | Lung | ND | [5] |
AIDS, catheter use | 3 (M) | No | No | Blood | Cure | [5] |
Parenteral nutrition, catheter use | 53 (F) | No | No | Blood | Cure | [5] |
ALL, catheter use | 5 (M) | No | No | Blood | Cure | [5] |
Injection drug use | 63 (M) | No | No | Endocarditis | Death | [5] |
Solid organ transplantation | 50 (F) | No | No | Endocarditis | ND | [5] |
Patients with PID | ||||||
CGD | 21 (F) | Yes | No | Lung | Cure | [14] |
CARD9 deficiency | 6 (F) | Yes | Yes | No | Relapse | This report |
Abbreviations: AIDS, acquired immunodeficiency syndrome; ALL, acute lymphoblastic leukemia; CAPD, continuous ambulatory peritoneal dialysis; CGD, chronic granulomatous disease; dig, digestive tract; F, female; LN, lymph node; M, male; mo, months; NA, not available; ND, not determined; PID, primary immunodeficiency disease.
a Multiplex family.