Table 1.
The 2008 WHO classification of myeloid neoplasms
Myeloproliferative Neoplasms |
Chronic myelogenous leukaemia, BCR-ABL1 positive |
Chronic neutrophilic leukaemia |
Polycythaemia vera |
Primary myelofibrosis |
Essential thrombocythaemia |
Chronic eosinophilic leukaemia, NOS |
Mastocytosis |
Myeloproliferative neoplasm, unclassifiable |
Myeloid and Lymphoid Neoplasms with Eosinophilia and Abnormalities of PDGFRA PDGFRB or FGFR1 |
Myelodyspastic/Myeloproliferative Neoplasms |
Chronic myelomonocytic leukaemia |
Atypical chronic myeloid leukaemia, BCR-ABL1 negative |
Juvenile myelomonocytic leukaemia |
Myelodysplastic/myeloproliferative neoplasm, unclassifiable |
Refractory anaemia with ring sideroblasts associated with marked thrombocytosis |
Myelodysplastic Syndromes |
Refractory cytopenia with unilineage dysplasia |
Refractory anaemia with ring sideroblasts |
Refractory cytopenia with multilineage dysplasia |
Refractory anaemia with excess blasts |
Myelodysplastic syndrome associated with isolated del(5q) |
Myelodysplastic syndrome, unclassifiable |
Childhood myelodysplastic syndrome |
Refarctory cytopenia of childhood |
Acute Myeloid Leukaemia (AML) and Related Precursor Neoplasms |
AML with recurrent genetic abnormalities |
AML with t(8;21)(q22;q22); RUNX1-RUNX1T1 |
AML with inv(16)(p13.1q22) or t(16;16)(p13.1;q22); CBFβ-MYH11 |
Acute promyelocytic leukemia with t(15;17)(q22;q12); PML-RARA |
AML with t(9;11)(p22;q23); MLLT3-MLL |
AML with t(6;9)(p23;q34); DEK-NUP214 |
AML with inv(3)(q21q26.2) or t(3;3)(q21;q26.2); RPN1-EVI1 |
AML (megakaryoblastic) with t(1;22)(p13;q13); RBM15-MKL1 |
Provisional entity: AML with mutated NPM1 |
Provisional entity: AML with mutated CEBPA |
AML with myelodysplasia-related changes |
Therapy-related myeloid neoplasms |
Acute myeloid leukaemia, not otherwise specified |
AML with minimal differentiation |
AML without maturation |
AML with maturation |
Acute myelomonocytic leukaemia |
Acute monoblastic and monocytic leukaemia |
Acute erythroid leukaemia |
Acute megakaryoblastic leukaemia |
Acute basophilic leukaemia |
Acute panmyelosis with myelofibrosis |
Myeloid sarcoma |
Myeloid proliferations related to Down syndrome |
Blastic plasmacytoid dendritic cell neoplasm |