Skip to main content
. 2015 Mar 30;7(6):695–713. doi: 10.15252/emmm.201404511

Table 2.

Improvement of 6-min walk test (6 MWT) in an ISCU mut/mut individual after initiation of pulmonary vasodilator therapy (PDE5 inhibitor)

Pulmonary vasodilator 6MW distance (meters)
None 240
Tadalafil (20 mg daily for 7 days followed by 40 mg daily for 40 days) 360
Tadalafil (20 mg daily for 7 days followed by 40 mg daily for 166 days) 364