Table 2.
Improvement of 6-min walk test (6 MWT) in an ISCU mut/mut individual after initiation of pulmonary vasodilator therapy (PDE5 inhibitor)
| Pulmonary vasodilator | 6MW distance (meters) |
|---|---|
| None | 240 |
| Tadalafil (20 mg daily for 7 days followed by 40 mg daily for 40 days) | 360 |
| Tadalafil (20 mg daily for 7 days followed by 40 mg daily for 166 days) | 364 |