Table 2.

Urinary GAGs in patients with mucopolysaccharidoses

Patient	Age (years)	Urine GAG (mg/mmol of creat)	Age matched reference range (mg/mmol of creat)
			Laboratory	Literature reference range [9]
1	1	67.8	7.6–29.7	9.1–29.9
2	2	26.2	10.0–24.0	7.7–21.3
3	3	21.6	10.0–24.0	7.7–21.3
4	4	49.4	9.9–17.1	7.6–14.4
5	5	114.6	9.9–17.1	7.6–14.4
6	6	46.3	8.0–18.5	5.7–12.9
7	6	31	8.0–18.5	5.7–12.9
8	8	51.5	6.9–13.0	5.2–11.6
9	9	15	6.9–13.0	5.2–11.6
10	12	35	1.0–7.7	1.5–5.1