. Author manuscript; available in PMC: 2015 Jun 19.

Published in final edited form as: J Pediatr. 2013 Dec 22;164(5):1121–1127.e1. doi: 10.1016/j.jpeds.2013.11.033

Table II.

Heart defect classifications

Cyanotic heart defects
TGA	8 TGA
HLHS	5 HLHS
	1 HLHS + DORV + mitral atresia
Single ventricle	1 Tricuspid atresia + VSD
Single ventricle with coarctation of the aorta	1 DORV + atrioventricular canal defect + coarctation
	1 DORV + VSD + coarctation
	1 DILV + L-TGA + aortic stenosis
Single ventricle with pulmonary stenosis/atresia	1 DORV + hypoplastic right heart + pulmonary stenosis
	1 DORV + ventricular inversion + pulmonary stenosis
	1 Pulmonary atresia + hypoplastic right heart
	1 DILV + L-TGA + pulmonary stenosis
	1 Single ventricle + pulmonary atresia with heterotaxy
	1 Tricuspid atresia + VSD + pulmonary stenosis
2 ventricles	2 Tetralogy of Fallot (SP_O₂ <80)
Acyanotic heart defects
2 Ventricles	2 Tetralogy of Fallot (SP_O₂ >80)
	1 VSD
	1 Truncus arteriosus
2 Ventricles with coarctation of the aorta	2 Coarctation + mitral stenosis
	1 VSD + coarctation
	1 VSD + interrupted aortic arch
	1 Ebstein anomaly + VSD + coarctation + left ventricle dysfunction

DILV, double inlet left ventricle; DORV, double outlet right ventricle; HLHS, hypoplastic left heart syndrome; L-TGA, levo-transposition of the great arteries; SPO₂, blood oxygen saturation; TGA, transposition of the great arteries; VSD, ventricular septal defect.